Predicted to enable copper chaperone activity and copper ion binding activity. Predicted to be involved in mitochondrial cytochrome c oxidase assembly. Predicted to be located in mitochondrial inner membrane. Used to study mitochondrial metabolism disease. Human ortholog(s) of this gene implicated in hypertrophic cardiomyopathy; mitochondrial complex IV deficiency nuclear type 2; and myopia. Is an ortholog of human SCO1 (synthesis of cytochrome C oxidase 1).