Enables protein xylosyltransferase activity. Involved in several processes, including UDP-D-xylose metabolic process; egg-laying behavior; and glycosaminoglycan biosynthetic process. Predicted to be located in Golgi membrane and endoplasmic reticulum membrane. Human ortholog(s) of this gene implicated in Desbuquois dysplasia; pseudoxanthoma elasticum; and type 1 diabetes mellitus. Is an ortholog of human XYLT1 (xylosyltransferase 1).
Predicted to enable unfolded protein binding activity. Predicted to be involved in protein folding. Predicted to be located in cytoplasm. Predicted to be part of prefoldin complex. Is an ortholog of human PFDN4 (prefoldin subunit 4).